Patterns of care and outcome of CIC-rearranged sarcoma patients: A nationwide study of the French sarcoma group.
Fiche publication
Date publication
décembre 2022
Journal
Cancer medicine
Auteurs
Membres identifiés du Cancéropôle Est :
Dr GANTZER Justine
Tous les auteurs :
Brahmi M, Gaspar N, Gantzer J, Toulmonde M, Boudou-Rouquette P, Bompas E, Firmin N, Valentin T, Cancel M, Duffaud F, Bertucci F, Perrin C, Dufresne A, Marec-Bérard P, Jean-Denis M, Ray-Coquard I, Le Loarer F, Pierron G, Tirode F, Blay JY, Watson S
Lien Pubmed
Résumé
CIC-rearranged sarcomas (CIC-RS) represent the most frequent subset of "Ewing-like" undifferentiated small round cell sarcomas. These tumors tend to be more aggressive than Ewing sarcomas. Moreover, treatment strategy can differ according to teams. The primary aim of this retrospective study was to describe the characteristics, treatments, and outcome for patients with CIC-RS included in the French NETSARC+ database.
Mots clés
CIC-rearranged sarcomas, CIC::DUX4 sarcomas, Ewing-like sarcoma., Ultra-rare sarcoma, Undifferentiated round cell sarcoma
Référence
Cancer Med. 2022 12 20;: