The spectrum of orofacial manifestations in systemic sclerosis: a challenging management.

Fiche publication


Date publication

mai 2017

Journal

Oral diseases

Auteurs

Membres identifiés du Cancéropôle Est :
Pr MARTIN Thierry


Tous les auteurs :
Jung S, Martin T, Schmittbuhl M, Huck O

Résumé

Systemic sclerosis (SSc) is a rare multisystem connective tissue disorder characterized by the triad fibrosis, vasculopathy and immune dysregulation. This chronic disease has a significant impact on the orofacial region that is involved in more than two-thirds of the cases. SSc patients can show a wide array of oral manifestations, which are usually associated with a severe impairment of the quality of life. They often present a decreased the salivary flow and a reduced mouth opening that contribute substantially to the worsening of the oral health status. Therefore, SSc patients require specific and multidisciplinary interventions that should be initiated as early as possible. The identification of specific radiological and clinical signs at the early stage will improve the management of such patients. This study reviews the wide spectrum of orofacial manifestations associated with SSc and suggests clues for the oral management that remains challenging.

Mots clés

fibrosis, oral management, orofacial manifestations, systemic sclerosis

Référence

Oral Dis. 2017 May;23(4):424-439