Systemic capillary leak syndrome and autoimmune diseases: A case series.
Fiche publication
Date publication
février 2017
Journal
Seminars in arthritis and rheumatism
Auteurs
Membres identifiés du Cancéropôle Est :
Pr WEBER Jean-Christophe
Tous les auteurs :
Guffroy A, Dervieux B, Gravier S, Martinez C, Deibener-Kaminsky J, Hachulla E, Michel M, Weber JC, Korganow AS, Arnaud L, Gottenberg JE, Sibilia J,
Lien Pubmed
Résumé
Systemic capillary leak syndrome (Clarkson's disease) is a rare entity characterized by recurrent and unpredictable attacks of capillary leakage of plasma fluid and proteins throughout the endothelium. Some cases are secondary. We describe the rare association between secondary capillary leak syndrome (SCLS) and autoimmune diseases.
Mots clés
Anti-Ro/SSA, Sjögren, Autoimmunity, Capillary leak syndrome, Inflammatory myopathy, Systemic sclerosis
Référence
Semin. Arthritis Rheum.. 2017 Feb;46(4):509-512