Schnitzler syndrome: validation and applicability of diagnostic criteria in real-life patients.
Fiche publication
Date publication
février 2017
Journal
Allergy
Auteurs
Membres identifiés du Cancéropôle Est :
Pr AUBIN François, Pr LIPSKER Dan, Pr SAULEAU Erik-André, Pr GOTTENBERG Jacques-Eric
Tous les auteurs :
Gusdorf L, Asli B, Barbarot S, Néel A, Masseau A, Puéchal X, Gottenberg JE, Grateau G, Blanchard-Delaunay C, Rizzi R, Lifermann F, Kyndt X, Aubin F, Bessis D, Boye T, Gayet S, Rongioletti F, Sauleau E, Fermand JP, Lipsker D
Lien Pubmed
Résumé
Schnitzler syndrome is characterized by an urticarial rash, a monoclonal gammopathy, and clinical, histological, and biological signs of neutrophil-mediated inflammation. The aim of this study was to assess the applicability and validity of the existing diagnostic criteria in real-life patients.
Mots clés
Schnitzler syndrome, auto-inflammatory disease, diagnostic criteria, monoclonal gammopathy, neutrophilic urticarial dermatosis
Référence
Allergy. 2017 Feb;72(2):177-182