Severe elastic fiber fragmentation/loss is correlated with Marfan syndrome in patients with an ascending aortic aneurysm.

Fiche publication

Date publication

février 2026

Journal

Vascular diseases (Paris, France)

Auteurs

Membres identifiés du Cancéropôle Est :
Pr GAUCHOTTE Guillaume

Tous les auteurs :
Bakour N, Liu Y, Burcheri-Curatolo A, Benzha MY, Villemot JP, Maureira JP, Gauchotte G

Lien Pubmed

https://www.ncbi.nlm.nih.gov/pubmed/41748346

Résumé

Aortic wall degeneration was described by a consensus statement published in 2016 by the Society for Cardiovascular Pathology (SCP) and Association for European Cardiovascular Pathology (AECP). The aim of this study was to determine if histopathologic features could predict the presence of genetic syndrome, to assess the prognostic value of histological findings, and to correlate it with clinical data.