Pleuroparenchymal fibroelastosis.
Fiche publication
Date publication
juillet 2022
Journal
Current opinion in pulmonary medicine
Auteurs
Membres identifiés du Cancéropôle Est :
Pr BONNIAUD Philippe
Tous les auteurs :
Cottin V, Si-Mohamed S, Diesler R, Bonniaud P, Valenzuela C
Lien Pubmed
Résumé
Pleuroparenchymal fibroelastosis (PPFE) is a clinico-radiologic-pathologic interstitial lung disease (ILD) characterized by fibrosis that has upper lobe and subpleural predominance, involving both the visceral pleura and the subjacent subpleural lung parenchyma, and comprises dense fibroelastic changes with prominent elastosis of the alveolar walls together with fibrous thickening of the visceral pleura. The goal of this review is to summarize the state-of-the-art understanding in PPFE.
Référence
Curr Opin Pulm Med. 2022 07 19;: