Usual interstitial pneumonia in ANCA-associated vasculitis: A poor prognostic factor.

Fiche publication


Date publication

septembre 2019

Journal

Journal of autoimmunity

Auteurs

Membres identifiés du Cancéropôle Est :
Pr BONNOTTE Bernard, Dr DEVILLIERS Hervé, Pr BONNIAUD Philippe


Tous les auteurs :
Maillet T, Goletto T, Beltramo G, Dupuy H, Jouneau S, Borie R, Crestani B, Cottin V, Blockmans D, Lazaro E, Naccache JM, Pugnet G, Nunes H, de Menthon M, Devilliers H, Bonniaud P, Puéchal X, Mouthon L, Bonnotte B, Guillevin L, Terrier B, Samson M,

Résumé

Progressive fibrosing interstitial lung disease (ILD) is rarely associated with antineutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV). This study focused on the outcomes of ILD patients with associated AAV (AAV-ILD).

Mots clés

ANCA-Associated vasculitis, Interstitial lung disease, Non-specific interstitial pneumonia, Prognosis, Survival, Usual interstitial pneumonia

Référence

J. Autoimmun.. 2019 Sep 27;:102338