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Fiche publication


Date publication

mai 2018

Journal

Revue neurologique

Auteurs

Membres identifiés du Cancéropôle Est :
Dr DEVILLIERS Hervé


Tous les auteurs :
Brenière C, Blanc C, Devilliers H, Samson M, Delpont B, Bielefeld P, Besancenot JF, Giroud M, Béjot Y

Résumé

Behçet's disease is a rare multisystemic vasculitis with an etiology that is still unknown. Neurological manifestations may be seen in approximately 5-15% of patients, and both parenchymal and extraparenchymal neurological involvement has been described. When cerebral venous thrombosis (CVT) is the main extraparenchymal manifestation of Behçet's disease, the condition is then dubbed "angio-Behçet's syndrome". However, arterial involvement is extremely rare, with only one reported case of vasculo-neuro-Behçet's disease, characterized by both venous and intracranial arterial involvement - until now. This report is of two patients diagnosed with Behçet's disease characterized by the concomitant presence of both cerebral arterial manifestations and CVT.

Mots clés

Arterial aneurysm, Behçet's disease, Cerebral venous thrombosis, Ischemic stroke, Vasculo-Behçet's disease

Référence

Rev. Neurol. (Paris). 2018 May;174(5):337-341